Bilateral Renal Angiomyolipomas Giants
Renal angiomyolipoma is a rare benign mesenchymal neoplasm
and is characterized by the presence of thin dysmorphic vessels,
smooth muscle and adipose tissue.
The incidence of renal angiomyolipoma is 0.1-0.3% and it can be
presented as an isolated pathology or be associated
with other entities, such as Tuberous Sclerosis or Bourneville’s disease,
and Von Recklinghausen disease or neurofibromatosis.
We report a case of a female patient aged 22 with kidney angiolipomas
giant associated with tuberous sclerosis, syndrome characterized by
the formation of hamartomas and tumors in different organs of the body.
No hypertensive, diabetic or dyslipidemia. She described hours of evolution diffuse
abdominal pain without apparent cause, no hematuria or urinary symptoms.
No digestive disorders was observed. On physical examination it revealed
supraventricular tachycardia and soft abdomen with tenderness without location,
slight signs of peritoneal irritation and palpation of cysts.
Right renal fist percussion was positive.
Patient with tuberous sclerosis and severe bilateral nephromegaly
will occupy more spec in the abdominal cavity
leading to bilateral renal hamartomata’s.
A level mesograstrioempty right can be see none pseudo-capsular
formation of approximately 10 cm major axis sonographically
which corresponds to a clot.
Free fluid between intestinal loops and retroperitoneal due to
bleeding from the right renal vasculature.
Homogeneous splenomegaly about 15 cm major axis.
With multiple spinal bones window blastic lesions are
seen features of Bourneville disease.
Urol Androl Open J. 2016; 1(1): 15-17. doi: 10.17140/UAOJ-1-104
