An Unusual Intracranial Inflammatory Process of Unknown Origin

Abstract

We present an unusual case of steroid responsive inflammatory condition, involving sellar suprasellar
region with further ependymal lesions. This is complicated by previous surgery due to
pituitary adenoma, not thought to related to inflammatory process. The patient responded well
to steroids, but deteriorated due to development of hydrocephalus caused by obstruction due
to adhesions. Despite extensive literature review and consideration of all known pathological
conditions, it was concluded that the condition represented another inflammatory entity not yet
fully characterised. The case also highlights that despite the steroid responsive nature of the
condition, the ependymal involvement can result in progressive acute obstructive hydrocephalus
with clinical deterioration. This case also suggests close follow-up and early imaging for
early detection and treatment of this complication.